Tests for assessing disease development and the patient's condition
Six-Minute Walk Test
This is a functional walk test which measures how far a patient can walk in six minutes. The test is used to assess and evaluate functional status. The result is presented as a percentage of the expected distance for a six-minute walk, based on age and gender-matched healthy individuals.
This is a functional walk test which measures how far a patient can walk in six minutes. The test is used to assess and evaluate functional status. The result is presented as a percentage of the expected distance for a six-minute walk, based on age and gender-matched healthy individuals.
BOT-2 (Bruininks-Oseretsky Test of Motor Proficiency, 2nd edition)
BOT-2 is a standardised test of motor proficiency, which measures fine and gross motor skills in individuals aged 4 to 21.
BOT-2 comprises 4 parts:
BOT-2 is a standardised test of motor proficiency, which measures fine and gross motor skills in individuals aged 4 to 21.
BOT-2 comprises 4 parts:
- Fine motor response
- Arm and hand co-ordination
- Body co-ordination
- Strength and dexterity
PDMS-2 (Peabody Development Motor Scales, 2nd edition)
PDMS-2 is a normed, standardised instrument that assesses fine and gross motor skills of children. The scale is designed for younger children – from birth up to age 5 – with suspected motor retardation.
PDMS-2 comprises 6 subtests:
PDMS-2 is a normed, standardised instrument that assesses fine and gross motor skills of children. The scale is designed for younger children – from birth up to age 5 – with suspected motor retardation.
PDMS-2 comprises 6 subtests:
- Reflexes (measures the child’s ability to automatically react to events in his/her environment)
- Stationary (measures the child’s ability to sustain control of his/her body and stay in balance
- Locomotion (measures the child’s ability to move from one place to another)
- Object Manipulation (measures a child’s ability to handle balls, e.g. catching, throwing and kicking)
- Grasping (measures the child’s ability to use his/her hands)
- Visual Motor Integration (measures the child’s ability to use his/her visual and perceptual skills to perform complex eye-hand co-ordination tasks)
Clinical Assessment Tool and questionnaire for the patient/carer
The HPP Clinical Assessment Tool includes examples of a wide variety of tests and makes the asssessment of the disease development easier. The tests are categorised by symptoms or organs, to make it easy to find the most relevant test for the individual patient and his/her situation.
Accompanying the tool is a questionnaire which the patient (or carer) can complete ahead of each appointment. This can then be used as a foundation when discussing the patient’s life situation and everyday life.
Download the tool Download the questionnaire (for adults)
Download the questionnaire (for carers to children)
Download explanation of tests
Download the questionnaire (for carers to children)
Download explanation of tests
Leung EC et al. JIMD Rep 2013; 11: 73-78.
Mornet E. Best Pract Res Clin Rheum 2008; 22: 113-127.
Mornet E et al. Ann Hum Genet 2011; 75: 439-445.
Rockman-Greenberg C. Ped Endocrinol Rev 2013; 10 (Suppl 2): 380-388.
Whyte MP. Ann N Y Acad Sci 2010; 1192: 190-200.
Goemans N et al. PLoS One. 2013;8(12):e84120
Deitz JC et al., Phys Occup Ther Pediatr. 2007;27(4):87–102
Folio R et al. Peabody Developmental Motor Scales-2 (2nd ed.). Austin, TX: Pro-Ed; 2000.
Mornet E. Best Pract Res Clin Rheum 2008; 22: 113-127.
Mornet E et al. Ann Hum Genet 2011; 75: 439-445.
Rockman-Greenberg C. Ped Endocrinol Rev 2013; 10 (Suppl 2): 380-388.
Whyte MP. Ann N Y Acad Sci 2010; 1192: 190-200.
Goemans N et al. PLoS One. 2013;8(12):e84120
Deitz JC et al., Phys Occup Ther Pediatr. 2007;27(4):87–102
Folio R et al. Peabody Developmental Motor Scales-2 (2nd ed.). Austin, TX: Pro-Ed; 2000.
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